
High-Yield Clinical Immunology: Primary Immunodeficiencies -3 (Disorders of Adaptive Immune System : B-cell and/or T cell Immunodeficiencies)
Erly Brialdia Okomo
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<p>We discuss the following disorders of adaptive immune system resulting in primary immunodeficiency: <br> B-cell disorders: Agammaglobulinemia (including Bruton's), Selective IG deficiency (including selective IgA deficiency), Common Variable Immunodeficiency</p> <p>T-cell Disorders: DiGeroge, IL-12 receptor pathway disorders (Mendelian Susceptibility to Mycobacterial Infection), Chronic Mucocutaneous Candidiasis</p> <p>Combined B & T cell disorders: Severe combined immunodeficiency (SCID), Autosomal- Dominant Hyper-IgE Syndrome, Wiskott-Aldrich, Ataxia-Telangiectasia, Hyper-IgM syndrome</p>
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High-Yield Clinical Immunology: Primary Immunodeficiencies -3 (Disorders of Adaptive Immune System : B-cell and/or T cell Immunodeficiencies)
Erly Brialdia Okomo